Abstract: 【Abstract】 Objective To investigate the clinical characteristics of pulmonary hilum Castleman’s disease. Methods 　The clinical characteristics of 4 patients diagnosed with pulmonary hilum Castleman’s disease in our department were analysed and compared with findings in relevant literature. Results 　Gender and age were not associated with Castleman's disease. The disease was often identified in physical examinations with atypical clinical symptoms. Chest CT was the most common and valuable diagnostic method revealing soft tissue mass near the pulmonary hilum. Gross-total resection of the tumor and (or) lobectomy through a combined posterior trans-thoracic approach were commonly performed, with good prognosis. Conclusion 　 Hilum Castleman's disease can be effectively diagnosed and treated.